Double-outlet right ventricle (DORV) is a congenital heart defect where two major arteries, the aorta (which carries blood to the body) and the pulmonary artery (which carries blood to the lungs), are not connected as they should be in the heart. Normally, the aorta connects to the left lower heart chamber, while the pulmonary artery connects to the right lower chamber. But in babies with DORV, both arteries partially or fully connect to the right lower heart chamber, creating a hole between the lower chambers called a ventricular septal defect (VSD). This leads to a mixing of oxygen-rich and oxygen-poor blood, causing symptoms like skin discoloration.
Symptoms of DORV usually appear in the first few weeks after birth. Most infants born with DORV need open-heart surgery within their first year to fix the heart’s malformation and improve blood flow. Additionally, DORV can sometimes occur along with other heart issues, like additional defects or problems with heart valves or blood vessels. This makes it important for affected infants to receive comprehensive medical evaluation and treatment.
In DORV, there’s always a VSD (hole in the septum between the ventricles). This hole allows blood to flow between the ventricles. DORV can be categorized based on the location of the VSD:
Symptoms of DORV (Double Outlet Right Ventricle) typically become noticeable shortly after birth and resemble those of other congenital heart conditions. These signs may include:
In addition to these symptoms, infants with DORV may have other associated congenital issues, such as:
The exact cause of DORV is not fully understood, but it can occur in babies with chromosomal abnormalities.
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